M35.0Sjogren syndrome

M35.0 is the ICD-10-CM diagnosis code for Sjogren syndrome. It belongs to category M35 (other systemic involvement of connective tissue), block M30-M36 (systemic connective tissue disorders) and chapter 13 (diseases of the musculoskeletal system and connective tissue). It is a header code, so it can't be reported by itself; one of its 13 subcodes must be used instead.

Within M35 (other systemic involvement of connective tissue), M35.0 is specifically for Sjogren syndrome. Related codes cover other overlap syndromes (M35.1), Behcet's disease (M35.2), polymyalgia rheumatica (M35.3), diffuse (eosinophilic) fasciitis (M35.4), multifocal fibrosclerosis (M35.5), relapsing panniculitis [Weber-Christian] (M35.6), hypermobility syndrome (M35.7), other specified systemic involvement of connective tissue (M35.8) and 1 more.

To report this condition, pick the subcode that matches the documentation: M35.00 (unspecified), M35.01 (with keratoconjunctivitis), M35.02 (with lung involvement), M35.03 (with myopathy), M35.04 (with tubulo-interstitial nephropathy), M35.05 (with inflammatory arthritis), M35.06 (with peripheral nervous system involvement), M35.07 (with central nervous system involvement) and 5 more.

Don't report M35.0 together with the conditions in its Excludes1 note: dry mouth, unspecified (R68.2).

Use an additional code to identify associated manifestations.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015, and changed in FY2022 (title revised).