Q07.0Arnold-Chiari syndrome

Q07.0 is the ICD-10-CM diagnosis code for Arnold-Chiari syndrome. It belongs to category Q07 (other congenital malformations of nervous system), block Q00-Q07 (congenital malformations of the nervous system) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is a header code, so it can't be reported by itself; one of its 4 subcodes must be used instead.

Within Q07 (other congenital malformations of nervous system), Q07.0 is specifically for Arnold-Chiari syndrome. Related codes cover other specified congenital malformations of nervous system (Q07.8) and congenital malformation of nervous system, unspecified (Q07.9).

To report this condition, pick the subcode that matches the documentation: Q07.00 (without spina bifida or hydrocephalus), Q07.01 (with spina bifida), Q07.02 (with hydrocephalus) and Q07.03 (with spina bifida and hydrocephalus).

Don't report Q07.0 together with the conditions in its Excludes1 note: Arnold-Chiari syndrome, type III (Q01.-) and Arnold-Chiari syndrome, type IV (Q04.8).

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.