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ICD-10-CM 2027 diagnosis code

Q85.0Neurofibromatosis (nonmalignant)

Not billable — use a more specific code

Q85.0 is a header code, so it can't be reported by itself. Choose one of the 5 more specific codes beneath it.

Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About Q85.0

Q85.0 is the ICD-10-CM diagnosis code for neurofibromatosis (nonmalignant). It belongs to category Q85 (phakomatoses, not elsewhere classified), block Q80-Q89 (other congenital malformations) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is a header code, so it can't be reported by itself; one of its 5 subcodes must be used instead.

Within Q85 (phakomatoses, not elsewhere classified), Q85.0 is specifically for neurofibromatosis (nonmalignant). Related codes cover Tuberous sclerosis (Q85.1), other phakomatoses, not elsewhere classified (Q85.8) and Phakomatosis, unspecified (Q85.9).

To report this condition, pick the subcode that matches the documentation: Q85.00 (unspecified), Q85.01 (1), Q85.02 (2), Q85.03 (Schwannomatosis) and Q85.09 (neurofibromatosis).

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Specific codes under Q85.0

Notes that apply from higher levels

Instructions written at a parent level also apply to Q85.0.

› From Q85 Phakomatoses, not elsewhere classified
Excludes1
  • ataxia telangiectasia [Louis-Bar] (G11.3)
  • familial dysautonomia [Riley-Day] (G90.1)

Broader instructions also apply from Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders.

Codes whose notes reference Q85.0

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
  • No changes since FY2016.

Common questions about Q85.0

Is Q85.0 billable?

No. Q85.0 is a header code. Report one of its more specific subcodes instead.