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ICD-10-CM 2027 diagnosis code

Q07.01Arnold-Chiari syndrome with spina bifida

✓ Billable / specificPOA exempt

Q07.01 is a valid, billable ICD-10-CM code for arnold-chiari syndrome with spina bifida. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.

Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About Q07.01

Q07.01 is the ICD-10-CM diagnosis code for Arnold-Chiari syndrome with spina bifida. It belongs to category Q07 (other congenital malformations of nervous system), block Q00-Q07 (congenital malformations of the nervous system) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within Q07.0 (Arnold-Chiari syndrome), Q07.01 is specifically for Arnold-Chiari syndrome with spina bifida. Related codes cover without spina bifida or hydrocephalus (Q07.00), with hydrocephalus (Q07.02) and with spina bifida and hydrocephalus (Q07.03).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239), DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), DRG 791 (Prematurity with Major Problems, relative weight 4.1075) and DRG 793 (Full Term Neonate with Major Problems, relative weight 4.2195), in MDC 01 (Diseases and Disorders of the Nervous System) and MDC 15 (Newborns and Other Neonates with Conditions Originating in the Perinatal Period), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 741.90 (spina bifida without mention of hydrocephalus, unspecified region).

Notes that apply from higher levels

Instructions written at a parent level also apply to Q07.01.

› From Q07.0 Arnold-Chiari syndrome
Excludes1
  • Arnold-Chiari syndrome, type III (Q01.-)
  • Arnold-Chiari syndrome, type IV (Q04.8)
› From Q07 Other congenital malformations of nervous system
Excludes2
  • congenital central alveolar hypoventilation syndrome (G47.35)
  • familial dysautonomia [Riley-Day] (G90.1)
  • neurofibromatosis (nonmalignant) (Q85.0-)

Broader instructions also apply from Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders.

Alphabetic index entries

3 entries

Terms in the official ICD-10-CM index that lead to Q07.01.

MS-DRG v44.0 grouping

All DRGs →

Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.

MDC 15 · Newborns and Other Neonates with Conditions Originating in the Perinatal Period

MDC 15 · Newborns and Other Neonates with Conditions Originating in the Perinatal Period

ICD-9-CM equivalent

Converter →
  • 741.90Spina bifida without mention of hydrocephalus, unspecified regionapproximate

From the CMS 2018 General Equivalence Mappings (GEMs), the final GEMs release.

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
  • No changes since FY2016.

Common questions about Q07.01

Is Q07.01 billable?

Yes. Q07.01 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can Q07.01 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict Q07.01 as a principal diagnosis.

Is Q07.01 a CC or MCC?

No. Q07.01 is neither a CC nor an MCC under MS-DRG v44.0.

What DRG does Q07.01 group to?

Q07.01 is used in the MS-DRG v44.0 logic for MS-DRG 091 (Other Disorders of Nervous System with MCC), MS-DRG 092 (Other Disorders of Nervous System with CC), MS-DRG 093 (Other Disorders of Nervous System without CC/MCC), MS-DRG 791 (Prematurity with Major Problems) and MS-DRG 793 (Full Term Neonate with Major Problems). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.

What is the ICD-9 code for Q07.01?

The CMS General Equivalence Mappings map Q07.01 to ICD-9-CM 741.90.