Q85.09Other neurofibromatosis

Q85.09 is the ICD-10-CM diagnosis code for other neurofibromatosis. It belongs to category Q85 (phakomatoses, not elsewhere classified), block Q80-Q89 (other congenital malformations) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within Q85.0, choose Q85.09 (Other neurofibromatosis) only when documentation doesn't support a more specific option: neurofibromatosis, unspecified (Q85.00), neurofibromatosis, type 1 (Q85.01), neurofibromatosis, type 2 (Q85.02) and Schwannomatosis (Q85.03).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239) and DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 237.79 (other neurofibromatosis).