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ICD-10-CM 2027 diagnosis code

Q87.ALoeys-Dietz syndrome

✓ Billable / specificNew for 2027POA exemptCC — complication/comorbidity

Q87.A is a valid, billable ICD-10-CM code for loeys-dietz syndrome. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.

Code last changed in FY2027 (effective October 1, 2026). Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About Q87.A

Q87.A is the ICD-10-CM diagnosis code for Loeys-Dietz syndrome. It belongs to category Q87 (other specified congenital malformation syndromes affecting multiple systems), block Q80-Q89 (other congenital malformations) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within Q87 (other specified congenital malformation syndromes affecting multiple systems), Q87.A is specifically for Loeys-Dietz syndrome. Related codes cover congenital malformation syndromes predominantly affecting facial appearance (Q87.0), congenital malformation syndromes predominantly associated with short stature (Q87.1), congenital malformation syndromes predominantly involving limbs (Q87.2), congenital malformation syndromes involving early overgrowth (Q87.3), Marfan syndrome (Q87.4), other congenital malformation syndromes with other skeletal changes (Q87.5) and other specified congenital malformation syndromes, not elsewhere classified (Q87.8).

Don't report Q87.A together with the conditions in its Excludes1 note: arterial tortuosity syndrome (Q87.82), Ehlers-Danlos syndrome (Q79.6), Marfan syndrome (Q87.40-Q87.43) and other systemic involvement of connective tissue (M35).

Use an additional code(s) to identify all associated manifestations.

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 564 (Other Musculoskeletal System and Connective Tissue Diagnoses with MCC, relative weight 1.4908), DRG 565 (Other Musculoskeletal System and Connective Tissue Diagnoses with CC, relative weight 0.9783) and DRG 566 (Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC, relative weight 0.7378), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.

It was added in FY2027, effective October 1, 2026.

Coding notes

Excludes1Not coded here — never report together with this code
  • arterial tortuosity syndrome (Q87.82)
  • Ehlers-Danlos syndrome (Q79.6)
  • Marfan syndrome (Q87.40-Q87.43)
  • other systemic involvement of connective tissue (M35)

Notes that apply from higher levels

Instructions written at a parent level also apply to Q87.A.

› From Q87 Other specified congenital malformation syndromes affecting multiple systems
Use additional code
  • code(s) to identify all associated manifestations

Broader instructions also apply from Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders.

Alphabetic index entries

1 entries

Terms in the official ICD-10-CM index that lead to Q87.A.

MS-DRG v44.0 grouping

All DRGs →

Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2027 (effective 10/1/2026): Added

Common questions about Q87.A

Is Q87.A billable?

Yes. Q87.A is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can Q87.A be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict Q87.A as a principal diagnosis.

Is Q87.A a CC or MCC?

Q87.A is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.

What DRG does Q87.A group to?

Q87.A is used in the MS-DRG v44.0 logic for MS-DRG 564 (Other Musculoskeletal System and Connective Tissue Diagnoses with MCC), MS-DRG 565 (Other Musculoskeletal System and Connective Tissue Diagnoses with CC) and MS-DRG 566 (Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.

Did Q87.A change for 2027?

Yes. For FY2027 (effective October 1, 2026) it was added to the code set.