Q89.0Congenital absence and malformations of spleen

Q89.0 is the ICD-10-CM diagnosis code for congenital absence and malformations of spleen. It belongs to category Q89 (other congenital malformations, not elsewhere classified), block Q80-Q89 (other congenital malformations) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is a header code, so it can't be reported by itself; one of its 2 subcodes must be used instead.

Within Q89 (other congenital malformations, not elsewhere classified), Q89.0 is specifically for congenital absence and malformations of spleen. Related codes cover congenital malformations of adrenal gland (Q89.1), congenital malformations of other endocrine glands (Q89.2), Situs inversus (Q89.3), conjoined twins (Q89.4), multiple congenital malformations, not elsewhere classified (Q89.7), other specified congenital malformations (Q89.8) and congenital malformation, unspecified (Q89.9).

To report this condition, pick the subcode that matches the documentation: Q89.01 ((congenital)) and Q89.09 (spleen).

Don't report Q89.0 together with the conditions in its Excludes1 note: isomerism of atrial appendages (with asplenia or polysplenia) (Q20.6).

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.