Q89.1Congenital malformations of adrenal gland

Q89.1 is the ICD-10-CM diagnosis code for congenital malformations of adrenal gland. It belongs to category Q89 (other congenital malformations, not elsewhere classified), block Q80-Q89 (other congenital malformations) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within Q89 (other congenital malformations, not elsewhere classified), Q89.1 is specifically for congenital malformations of adrenal gland. Related codes cover congenital absence and malformations of spleen (Q89.0), congenital malformations of other endocrine glands (Q89.2), Situs inversus (Q89.3), conjoined twins (Q89.4), multiple congenital malformations, not elsewhere classified (Q89.7), other specified congenital malformations (Q89.8) and congenital malformation, unspecified (Q89.9).

Don't report Q89.1 together with the conditions in its Excludes1 note: adrenogenital disorders (E25.-) and congenital adrenal hyperplasia (E25.0).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 643 (Endocrine Disorders with MCC, relative weight 1.6139), DRG 644 (Endocrine Disorders with CC, relative weight 1.0044) and DRG 645 (Endocrine Disorders without CC/MCC, relative weight 0.7459), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 759.1 (anomalies of adrenal gland).