ICD-10 code for constitutional hyperbilirubinemia

The ICD-10-CM code for constitutional hyperbilirubinemia is E80.6 (Other disorders of bilirubin metabolism).

Within E80, choose E80.6 (Other disorders of bilirubin metabolism) only when documentation doesn't support a more specific option: hereditary erythropoietic porphyria (E80.0), porphyria cutanea tarda (E80.1), other and unspecified porphyria (E80.2), defects of catalase and peroxidase (E80.3), Gilbert syndrome (E80.4), Crigler-Najjar syndrome (E80.5) and disorder of bilirubin metabolism, unspecified (E80.7).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 441 (Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis with MCC, relative weight 1.8219), DRG 442 (Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis with CC, relative weight 0.9602) and DRG 443 (Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis without CC/MCC, relative weight 0.6885), in MDC 07 (Diseases and Disorders of the Hepatobiliary System and Pancreas), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.