ICD-10 code for Kimura disease

The ICD-10-CM code for Kimura disease is D21.9 (Benign neoplasm of connective and other soft tissue, unspecified).

Within D21, choose D21.9 (tissue, unspecified) only when documentation doesn't support a more specific option: tissue of head, face and neck (D21.0), tissue of upper limb, including shoulder (D21.1), tissue of lower limb, including hip (D21.2), tissue of thorax (D21.3), tissue of abdomen (D21.4), tissue of pelvis (D21.5) and tissue of trunk, unspecified (D21.6).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 564 (Other Musculoskeletal System and Connective Tissue Diagnoses with MCC, relative weight 1.4908), DRG 565 (Other Musculoskeletal System and Connective Tissue Diagnoses with CC, relative weight 0.9783) and DRG 566 (Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC, relative weight 0.7378), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.