ICD-10-CM 2027
ICD-10 code for papillary ependymoma
From the official ICD-10-CM alphabetic index entry “Ependymoma (epithelial) (malignant) › papillary”. Page updated September 29, 2026.
About coding papillary ependymoma
The ICD-10-CM code for papillary ependymoma is D43.2 (Neoplasm of uncertain behavior of brain, unspecified). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on D43.2.
Within D43, choose D43.2 (brain, unspecified) only when documentation doesn't support a more specific option: brain, supratentorial (D43.0), brain, infratentorial (D43.1), cranial nerves (D43.3), spinal cord (D43.4), other specified parts of central nervous system (D43.8) and central nervous system, unspecified (D43.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 054 (Nervous System Neoplasms with MCC, relative weight 1.5194) and DRG 055 (Nervous System Neoplasms without MCC, relative weight 1.0296), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific papillary ependymoma codes (official index)
- specified site
- unspecified site D43.2 — Neoplasm of uncertain behavior of brain, unspecified
Common questions about papillary ependymoma ICD-10 codes
What is the ICD-10 code for papillary ependymoma?
- D43.2 — Neoplasm of uncertain behavior of brain, unspecified. More specific codes apply when the documentation supports them: D43.2.
Is D43.2 billable?
- Yes. D43.2 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D43.2 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D43.2 as a principal diagnosis.
Is D43.2 a CC or MCC?
- No. D43.2 is neither a CC nor an MCC under MS-DRG v44.0.