ICD-10-CM 2027
ICD-10 code for pulmonary anomaly
From the official ICD-10-CM alphabetic index entry “Anomaly, anomalous (congenital) (unspecified type) › pulmonary”. Page updated September 29, 2026.
About coding pulmonary anomaly
The ICD-10-CM code for pulmonary anomaly is Q33.9 (Congenital malformation of lung, unspecified). The official index lists 11 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on Q33.9.
Within Q33, choose Q33.9 (Congenital malformation of lung, unspecified) only when documentation doesn't support a more specific option: congenital cystic lung (Q33.0), accessory lobe of lung (Q33.1), sequestration of lung (Q33.2), agenesis of lung (Q33.3), congenital bronchiectasis (Q33.4), ectopic tissue in lung (Q33.5), congenital hypoplasia and dysplasia of lung (Q33.6) and other congenital malformations of lung (Q33.8).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 205 (Other Respiratory System Diagnoses with MCC, relative weight 1.8244) and DRG 206 (Other Respiratory System Diagnoses without MCC, relative weight 0.9257), in MDC 04 (Diseases and Disorders of the Respiratory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific pulmonary anomaly codes (official index)
- artery NEC Q25.79 — Other congenital malformations of pulmonary artery
- valve Q22.3 — Other congenital malformations of pulmonary valve
- atresia Q22.0 — Pulmonary valve atresia
- insufficiency Q22.2 — Congenital pulmonary valve insufficiency
- specified type NEC Q22.3 — Other congenital malformations of pulmonary valve
- stenosis Q22.1 — Congenital pulmonary valve stenosis
- infundibular Q24.3 — Pulmonary infundibular stenosis
- subvalvular Q24.3 — Pulmonary infundibular stenosis
- venous connection Q26.4 — Anomalous pulmonary venous connection, unspecified
- partial Q26.3 — Partial anomalous pulmonary venous connection
- total Q26.2 — Total anomalous pulmonary venous connection
Common questions about pulmonary anomaly ICD-10 codes
What is the ICD-10 code for pulmonary anomaly?
- Q33.9 — Congenital malformation of lung, unspecified. More specific codes apply when the documentation supports them: Q25.79, Q22.3, Q22.0, Q22.2 and others below.
What is the ICD-10 code for artery nec pulmonary anomaly?
- Q25.79 — Other congenital malformations of pulmonary artery.
What is the ICD-10 code for valve pulmonary anomaly?
- Q22.3 — Other congenital malformations of pulmonary valve.
What is the ICD-10 code for venous connection pulmonary anomaly?
- Q26.4 — Anomalous pulmonary venous connection, unspecified.
Is Q33.9 billable?
- Yes. Q33.9 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q33.9 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q33.9 as a principal diagnosis.
Is Q33.9 a CC or MCC?
- No. Q33.9 is neither a CC nor an MCC under MS-DRG v44.0.