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ICD-10-CM 2027

ICD-10 code for Sirenomelia

Q87.2

Congenital malformation syndromes predominantly involving limbs

✓ Billable / specificCC — complication/comorbidity

From the official ICD-10-CM alphabetic index entry “Sirenomelia (syndrome)”. Page updated September 29, 2026.

About coding Sirenomelia

The ICD-10-CM code for Sirenomelia is Q87.2 (Congenital malformation syndromes predominantly involving limbs).

Within Q87 (other specified congenital malformation syndromes affecting multiple systems), Q87.2 is specifically for congenital malformation syndromes predominantly involving limbs. Related codes cover congenital malformation syndromes predominantly affecting facial appearance (Q87.0), congenital malformation syndromes predominantly associated with short stature (Q87.1), congenital malformation syndromes involving early overgrowth (Q87.3), Marfan syndrome (Q87.4), other congenital malformation syndromes with other skeletal changes (Q87.5), other specified congenital malformation syndromes, not elsewhere classified (Q87.8) and Loeys-Dietz syndrome (Q87.A).

Use an additional code(s) to identify all associated manifestations.

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

Common questions about Sirenomelia ICD-10 codes

What is the ICD-10 code for Sirenomelia?

Q87.2 — Congenital malformation syndromes predominantly involving limbs.

Is Q87.2 billable?

Yes. Q87.2 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can Q87.2 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict Q87.2 as a principal diagnosis.

Is Q87.2 a CC or MCC?

Q87.2 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.