ICD-10 code for spastic hereditary ataxia

The ICD-10-CM code for spastic hereditary ataxia is G11.4 (Hereditary spastic paraplegia).

Within G11 (hereditary ataxia), G11.4 is specifically for hereditary spastic paraplegia. Related codes cover congenital nonprogressive ataxia (G11.0), early-onset cerebellar ataxia (G11.1), Late-onset cerebellar ataxia (G11.2), cerebellar ataxia with defective DNA repair (G11.3), Hypomyelination - hypogonadotropic hypogonadism - hypodontia (G11.5), leukodystrophy with vanishing white matter disease (G11.6), other hereditary ataxias (G11.8) and unspecified (G11.9).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 058 (Multiple Sclerosis and Cerebellar Ataxia with MCC, relative weight 1.8438), DRG 059 (Multiple Sclerosis and Cerebellar Ataxia with CC, relative weight 1.2002) and DRG 060 (Multiple Sclerosis and Cerebellar Ataxia without CC/MCC, relative weight 0.9247), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.