G11.4Hereditary spastic paraplegia

G11.4 is the ICD-10-CM diagnosis code for hereditary spastic paraplegia. It belongs to category G11 (hereditary ataxia), block G10-G14 (systemic atrophies primarily affecting the central nervous system) and chapter 6 (diseases of the nervous system). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within G11 (hereditary ataxia), G11.4 is specifically for hereditary spastic paraplegia. Related codes cover congenital nonprogressive ataxia (G11.0), early-onset cerebellar ataxia (G11.1), Late-onset cerebellar ataxia (G11.2), cerebellar ataxia with defective DNA repair (G11.3), Hypomyelination - hypogonadotropic hypogonadism - hypodontia (G11.5), leukodystrophy with vanishing white matter disease (G11.6), other hereditary ataxias (G11.8) and unspecified (G11.9).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 058 (Multiple Sclerosis and Cerebellar Ataxia with MCC, relative weight 1.8438), DRG 059 (Multiple Sclerosis and Cerebellar Ataxia with CC, relative weight 1.2002) and DRG 060 (Multiple Sclerosis and Cerebellar Ataxia without CC/MCC, relative weight 0.9247), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 334.1 (hereditary spastic paraplegia).