ICD-10-CM 2027
ICD-10 code for von Willebrand disease
From the official ICD-10-CM alphabetic index entry “Disease, diseased › von Willebrand (-Jürgens) (angiohemophilia)”. Page updated September 29, 2026.
About coding von Willebrand disease
The ICD-10-CM code for von Willebrand disease is D68.00 (Von Willebrand disease, unspecified). The official index lists 12 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on D68.00.
Within D68.0, choose D68.00 (unspecified) only when documentation doesn't support a more specific option: type 1 (D68.01), type 2 (D68.02), type 3 (D68.03), acquired von Willebrand disease (D68.04) and other von Willebrand disease (D68.09).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 813 (Coagulation Disorders, relative weight 1.5257), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific von Willebrand disease codes (official index)
- acquired D68.04 — Acquired von Willebrand disease
- platelet-type D68.09 — Other von Willebrand disease
- pseudo D68.09 — Other von Willebrand disease
- specified NEC D68.09 — Other von Willebrand disease
- type 1 D68.01 — Von Willebrand disease, type 1
- type 1C D68.01 — Von Willebrand disease, type 1
- type 2 D68.029 — Von Willebrand disease, type 2, unspecified
- type 2A D68.020 — Von Willebrand disease, type 2A
- type 2B D68.021 — Von Willebrand disease, type 2B
- type 2M D68.022 — Von Willebrand disease, type 2M
- type 2N D68.023 — Von Willebrand disease, type 2N
- type 3 D68.03 — Von Willebrand disease, type 3
Common questions about von Willebrand disease ICD-10 codes
What is the ICD-10 code for von Willebrand disease?
- D68.00 — Von Willebrand disease, unspecified. More specific codes apply when the documentation supports them: D68.04, D68.09, D68.09, D68.09 and others below.
What is the ICD-10 code for acquired von willebrand disease?
- D68.04 — Acquired von Willebrand disease.
What is the ICD-10 code for platelet-type von willebrand disease?
- D68.09 — Other von Willebrand disease.
What is the ICD-10 code for pseudo von willebrand disease?
- D68.09 — Other von Willebrand disease.
What is the ICD-10 code for type 1 von willebrand disease?
- D68.01 — Von Willebrand disease, type 1.
What is the ICD-10 code for type 1c von willebrand disease?
- D68.01 — Von Willebrand disease, type 1.
What is the ICD-10 code for type 2 von willebrand disease?
- D68.029 — Von Willebrand disease, type 2, unspecified.
Is D68.00 billable?
- Yes. D68.00 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D68.00 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D68.00 as a principal diagnosis.
Is D68.00 a CC or MCC?
- D68.00 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.