ICD-10-CM 2027 diagnosis code
E71.1Other disorders of branched-chain amino-acid metabolism
E71.1 is a header code, so it can't be reported by itself. Choose one of the 3 more specific codes beneath it.
Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About E71.1
E71.1 is the ICD-10-CM diagnosis code for other disorders of branched-chain amino-acid metabolism. It belongs to category E71 (disorders of branched-chain amino-acid metabolism and fatty-acid metabolism), block E70-E88 (metabolic disorders) and chapter 4 (endocrine, nutritional and metabolic diseases). It is a header code, so it can't be reported by itself; one of its 3 subcodes must be used instead.
Within E71, choose E71.1 (Other disorders of branched-chain amino-acid metabolism) only when documentation doesn't support a more specific option: Maple-syrup-urine disease (E71.0), disorder of branched-chain amino-acid metabolism, unspecified (E71.2), disorders of fatty-acid metabolism (E71.3), disorders of carnitine metabolism (E71.4) and peroxisomal disorders (E71.5).
To report this condition, pick the subcode that matches the documentation: E71.11 (acidurias), E71.12 (metabolism) and E71.19 (metabolism).
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.
Specific codes under E71.1
Notes that apply from higher levels
Instructions written at a parent level also apply to E71.1.
Broader instructions also apply from E70-E88 Metabolic disorders and Chapter 4: Endocrine, nutritional and metabolic diseases.
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
- No changes since FY2016.
Common questions about E71.1
Is E71.1 billable?
- No. E71.1 is a header code. Report one of its more specific subcodes instead.