ICD-10-CM 2027 diagnosis code
E71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71 is a header code, so it can't be reported by itself. Choose one of the 6 more specific codes beneath it.Short description: Disord of branched-chain amino-acid metab & fatty-acid metab
Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About E71
E71 is the ICD-10-CM diagnosis code for disorders of branched-chain amino-acid metabolism and fatty-acid metabolism. It belongs to block E70-E88 (metabolic disorders) and chapter 4 (endocrine, nutritional and metabolic diseases). It is a header code, so it can't be reported by itself; one of its 6 subcodes must be used instead.
To report this condition, pick the subcode that matches the documentation: E71.0 (disease), E71.1 (metabolism), E71.2 (unspecified), E71.3 (metabolism), E71.4 (metabolism) and E71.5 (disorders).
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.
Specific codes under E71
- E71.0Maple-syrup-urine diseaseBillable
- E71.1Other disorders of branched-chain amino-acid metabolism
- E71.2Disorder of branched-chain amino-acid metabolism, unspecifiedBillable
- E71.3Disorders of fatty-acid metabolism
- E71.30Disorder of fatty-acid metabolism, unspecifiedBillable
- E71.31Disorders of fatty-acid oxidation
- E71.310Long chain/very long chain acyl CoA dehydrogenase deficiencyBillable
- E71.311Medium chain acyl CoA dehydrogenase deficiencyBillable
- E71.312Short chain acyl CoA dehydrogenase deficiencyBillable
- E71.313Glutaric aciduria type IIBillable
- E71.314Muscle carnitine palmitoyltransferase deficiencyBillable
- E71.318Other disorders of fatty-acid oxidationBillable
- E71.32Disorders of ketone metabolismBillable
- E71.39Other disorders of fatty-acid metabolismBillable
- E71.4Disorders of carnitine metabolism
- E71.5Peroxisomal disorders
Notes that apply from higher levels
Instructions written at a parent level also apply to E71.
Broader instructions also apply from E70-E88 Metabolic disorders and Chapter 4: Endocrine, nutritional and metabolic diseases.
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
- No changes since FY2016.
Common questions about E71
Is E71 billable?
- No. E71 is a header code. Report one of its more specific subcodes instead.