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Dx

ICD-10-CM 2027 · E70-E88

Metabolic disorders

Part of chapter 4, endocrine, nutritional and metabolic diseases.

About E70-E88

Block E70-E88 contains 17 categories and 286 billable codes for FY2027. No codes here changed in the FY2027 update. 3 codes are MCCs and 171 are CCs when reported as secondary diagnoses.

E70Disorders of aromatic amino-acid metabolism

E71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

E72Other disorders of amino-acid metabolism

E73Lactose intolerance

E74Other disorders of carbohydrate metabolism

E75Disorders of sphingolipid metabolism and other lipid storage disorders

E76Disorders of glycosaminoglycan metabolism

E77Disorders of glycoprotein metabolism

E78Disorders of lipoprotein metabolism and other lipidemias

E79Disorders of purine and pyrimidine metabolism

E80Disorders of porphyrin and bilirubin metabolism

E83Disorders of mineral metabolism

E84Cystic fibrosis

E85Amyloidosis

E86Volume depletion

E87Other disorders of fluid, electrolyte and acid-base balance

E88Other and unspecified metabolic disorders

Block notes

Excludes1
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
Excludes2
  • Ehlers-Danlos syndromes (Q79.6-)