ICD-10-CM 2027 diagnosis code
E74.03Cori disease
E74.03 is a valid, billable ICD-10-CM code for cori disease. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.
Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS, effective October 1, 2026. Updated September 29, 2026. About our data
About E74.03
E74.03 is the ICD-10-CM diagnosis code for Cori disease. It belongs to category E74 (other disorders of carbohydrate metabolism), block E70-E88 (metabolic disorders) and chapter 4 (endocrine, nutritional and metabolic diseases). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.
Within E74.0 (glycogen storage disease), E74.03 is specifically for Cori disease. Related codes cover unspecified (E74.00), von Gierke disease (E74.01), Pompe disease (E74.02), McArdle disease (E74.04), Lysosome-associated membrane protein 2 [LAMP2] deficiency (E74.05) and other glycogen storage disease (E74.09).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.
Before ICD-10, this condition was coded in ICD-9-CM as 271.0 (glycogenosis).
Coding notes
- Forbes disease
- Type III glycogen storage disease
Notes that apply from higher levels
Instructions written at a parent level also apply to E74.03.
Broader instructions also apply from E70-E88 Metabolic disorders and Chapter 4: Endocrine, nutritional and metabolic diseases.
Alphabetic index entries
12 entriesTerms in the official ICD-10-CM index that lead to E74.03.
- Amylopectinosis (brancher enzyme deficiency)
- Cori's disease (glycogen storage)
- Deficiency, deficient › brancher enzyme (amylopectinosis)
- Deficiency, deficient › debrancher enzyme (limit dextrinosis)
- Dextrinosis, limit (debrancher enzyme deficiency)
- Disease, diseased › Cori's (glycogenosis III)
- Disease, diseased › Forbes' (glycogenosis III)
- Disease, diseased › glycogen storage › Cori's
- Disease, diseased › glycogen storage › Forbes'
- Disease, diseased › glycogen storage › type III
- Forbes' glycogen storage disease
- Infiltrate, infiltration › liver › glycogen
MS-DRG v44.0 grouping
All DRGs →Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.
MDC 10 · Endocrine, Nutritional and Metabolic Diseases and Disorders
ICD-9-CM equivalent
Converter →- 271.0Glycogenosisapproximate
From the CMS 2018 General Equivalence Mappings (GEMs), the final GEMs release.
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
- No changes since FY2016.
Common questions about E74.03
Is E74.03 billable?
- Yes. E74.03 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E74.03 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E74.03 as a principal diagnosis.
Is E74.03 a CC or MCC?
- E74.03 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.
What DRG does E74.03 group to?
- E74.03 is used in the MS-DRG v44.0 logic for MS-DRG 642 (Inborn and Other Disorders of Metabolism). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.
What is the ICD-9 code for E74.03?
- The CMS General Equivalence Mappings map E74.03 to ICD-9-CM 271.0.