E74.1Disorders of fructose metabolism

E74.1 is the ICD-10-CM diagnosis code for disorders of fructose metabolism. It belongs to category E74 (other disorders of carbohydrate metabolism), block E70-E88 (metabolic disorders) and chapter 4 (endocrine, nutritional and metabolic diseases). It is a header code, so it can't be reported by itself; one of its 4 subcodes must be used instead.

Within E74 (other disorders of carbohydrate metabolism), E74.1 is specifically for disorders of fructose metabolism. Related codes cover glycogen storage disease (E74.0), disorders of galactose metabolism (E74.2), other disorders of intestinal carbohydrate absorption (E74.3), disorders of pyruvate metabolism and gluconeogenesis (E74.4), other specified disorders of carbohydrate metabolism (E74.8) and disorder of carbohydrate metabolism, unspecified (E74.9).

To report this condition, pick the subcode that matches the documentation: E74.10 (unspecified), E74.11 (fructosuria), E74.12 (intolerance) and E74.19 (metabolism).

Don't report E74.1 together with the conditions in its Excludes1 note: muscle phosphofructokinase deficiency (E74.09).

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.