ICD-10-CM 2027
ICD-10 code for ataxia
From the official ICD-10-CM alphabetic index entry “Ataxia, ataxy, ataxic”. Page updated September 29, 2026.
About coding ataxia
The ICD-10-CM code for ataxia is R27.0 (Ataxia, unspecified). The official index lists 48 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on R27.0.
Within R27, choose R27.0 (Ataxia, unspecified) only when documentation doesn't support a more specific option: other lack of coordination (R27.8) and unspecified lack of coordination (R27.9).
Don't report R27.0 together with the conditions in its Excludes1 note: ataxia following cerebrovascular disease (I69. with final characters -93).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
More specific ataxia codes (official index)
- acute R27.8 — Other lack of coordination
- autosomal recessive Friedreich G11.11 — Friedreich ataxia
- brain (hereditary) G11.9 — Hereditary ataxia, unspecified
- cerebellar (hereditary) G11.9 — Hereditary ataxia, unspecified
- with defective DNA repair G11.3 — Cerebellar ataxia with defective DNA repair
- alcoholic G31.2 — Degeneration of nervous system due to alcohol
- early-onset G11.10 — Early-onset cerebellar ataxia, unspecified
- with
- essential tremor G11.19 — Other early-onset cerebellar ataxia
- myoclonus [Hunt's ataxia] G11.19 — Other early-onset cerebellar ataxia
- retained tendon reflexes G11.19 — Other early-onset cerebellar ataxia
- in
- alcoholism G31.2 — Degeneration of nervous system due to alcohol
- myxedema E03.9 — Hypothyroidism, unspecified
- neoplastic disease D49.9 — Neoplasm of unspecified behavior of unspecified site
- specified disease NEC G32.81 — Cerebellar ataxia in diseases classified elsewhere
- late-onset (Marie's) G11.2 — Late-onset cerebellar ataxia
- cerebral (hereditary) G11.9 — Hereditary ataxia, unspecified
- congenital nonprogressive G11.0 — Congenital nonprogressive ataxia
- family, familial
- following
- cerebrovascular disease I69.993 — Ataxia following unspecified cerebrovascular disease
- cerebral infarction I69.393 — Ataxia following cerebral infarction
- intracerebral hemorrhage I69.193 — Ataxia following nontraumatic intracerebral hemorrhage
- nontraumatic intracranial hemorrhage NEC I69.293 — Ataxia following other nontraumatic intracranial hemorrhage
- specified disease NEC I69.893 — Ataxia following other cerebrovascular disease
- subarachnoid hemorrhage I69.093 — Ataxia following nontraumatic subarachnoid hemorrhage
- Friedreich's (heredofamilial) (cerebellar) (spinal) (with retained reflexes) G11.11 — Friedreich ataxia
- gait R26.0 — Ataxic gait
- hysterical F44.4 — Conversion disorder with motor symptom or deficit
- general R27.8 — Other lack of coordination
- gluten M35.9 — Systemic involvement of connective tissue, unspecified
- with celiac disease K90.0 — Celiac disease
- hereditary G11.9 — Hereditary ataxia, unspecified
- with neuropathy G60.2 — Neuropathy in association with hereditary ataxia
- cerebellar
- spastic G11.4 — Hereditary spastic paraplegia
- specified NEC G11.8 — Other hereditary ataxias
- spinal (Friedreich's) G11.11 — Friedreich ataxia
- heredofamilial
- Hunt's G11.19 — Other early-onset cerebellar ataxia
- hysterical F44.4 — Conversion disorder with motor symptom or deficit
- locomotor (progressive) (syphilitic) (partial) (spastic) A52.11 — Tabes dorsalis
- diabetic
- Marie's (cerebellar) (heredofamilial) (late- onset) G11.2 — Late-onset cerebellar ataxia
- nonorganic origin F44.4 — Conversion disorder with motor symptom or deficit
- nonprogressive, congenital G11.0 — Congenital nonprogressive ataxia
- psychogenic F44.4 — Conversion disorder with motor symptom or deficit
- Roussy-Lévy G60.0 — Hereditary motor and sensory neuropathy
- Sanger-Brown's (hereditary) G11.2 — Late-onset cerebellar ataxia
- spastic hereditary G11.4 — Hereditary spastic paraplegia
- spinal
- hereditary (Friedreich's) G11.11 — Friedreich ataxia
- progressive (syphilitic) A52.11 — Tabes dorsalis
- spinocerebellar, X-linked recessive G11.19 — Other early-onset cerebellar ataxia
- telangiectasia (Louis-Bar) G11.3 — Cerebellar ataxia with defective DNA repair
Don't confuse with (Excludes1 for R27.0)
- ataxia following cerebrovascular disease (I69. with final characters -93)
Common questions about ataxia ICD-10 codes
What is the ICD-10 code for ataxia?
- R27.0 — Ataxia, unspecified. More specific codes apply when the documentation supports them: R27.8, G11.11, G11.9, G11.9 and others below.
What is the ICD-10 code for acute ataxia?
- R27.8 — Other lack of coordination.
What is the ICD-10 code for autosomal recessive friedreich ataxia?
- G11.11 — Friedreich ataxia.
What is the ICD-10 code for brain ataxia?
- G11.9 — Hereditary ataxia, unspecified.
What is the ICD-10 code for cerebellar ataxia?
- G11.9 — Hereditary ataxia, unspecified.
What is the ICD-10 code for cerebral ataxia?
- G11.9 — Hereditary ataxia, unspecified.
What is the ICD-10 code for congenital nonprogressive ataxia?
- G11.0 — Congenital nonprogressive ataxia.
Is R27.0 billable?
- Yes. R27.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can R27.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict R27.0 as a principal diagnosis.
Is R27.0 a CC or MCC?
- No. R27.0 is neither a CC nor an MCC under MS-DRG v44.0.