ICD-10 code for hereditary ataxia

The ICD-10-CM code for hereditary ataxia is G11.9 (Hereditary ataxia, unspecified). The official index lists 4 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on G11.9.

Within G11, choose G11.9 (unspecified) only when documentation doesn't support a more specific option: congenital nonprogressive ataxia (G11.0), early-onset cerebellar ataxia (G11.1), Late-onset cerebellar ataxia (G11.2), cerebellar ataxia with defective DNA repair (G11.3), hereditary spastic paraplegia (G11.4), Hypomyelination - hypogonadotropic hypogonadism - hypodontia (G11.5), leukodystrophy with vanishing white matter disease (G11.6) and other hereditary ataxias (G11.8).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 058 (Multiple Sclerosis and Cerebellar Ataxia with MCC, relative weight 1.8438), DRG 059 (Multiple Sclerosis and Cerebellar Ataxia with CC, relative weight 1.2002) and DRG 060 (Multiple Sclerosis and Cerebellar Ataxia without CC/MCC, relative weight 0.9247), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.