ICD-10-CM 2027 diagnosis code
D55.0Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency
D55.0 is a valid, billable ICD-10-CM code for anemia due to glucose-6-phosphate dehydrogenase [g6pd] deficiency. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.Short description: Anemia due to glucose-6-phosphate dehydrogenase deficiency
Looking up by condition? See ICD-10 code for Favism.
Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About D55.0
D55.0 is the ICD-10-CM diagnosis code for anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency. It belongs to category D55 (anemia due to enzyme disorders), block D55-D59 (hemolytic anemias) and chapter 3 (diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.
Within D55 (anemia due to enzyme disorders), D55.0 is specifically for anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency. Related codes cover anemia due to other disorders of glutathione metabolism (D55.1), anemia due to disorders of glycolytic enzymes (D55.2), anemia due to disorders of nucleotide metabolism (D55.3), other anemias due to enzyme disorders (D55.8) and anemia due to enzyme disorder, unspecified (D55.9).
Don't report D55.0 together with the conditions in its Excludes1 note: glucose-6-phosphate dehydrogenase (G6PD) deficiency without anemia (D75.A).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 811 (Red Blood Cell Disorders with MCC, relative weight 1.3988) and DRG 812 (Red Blood Cell Disorders without MCC, relative weight 0.9234), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.
Before ICD-10, this condition was coded in ICD-9-CM as 282.2 (anemias due to disorders of glutathione metabolism).
Coding notes
- Favism
- G6PD deficiency anemia
- glucose-6-phosphate dehydrogenase (G6PD) deficiency without anemia (D75.A)
Notes that apply from higher levels
Instructions written at a parent level also apply to D55.0.
› From D55 Anemia due to enzyme disorders
- drug-induced enzyme deficiency anemia (D59.2)
Broader instructions also apply from Chapter 3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism.
Alphabetic index entries
11 entriesTerms in the official ICD-10-CM index that lead to D55.0.
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › Baghdad spring
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › deficiency › enzyme › glucose-6-phosphate dehydrogenase (G6PD)
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › deficiency › glucose-6-phosphate dehydrogenase
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › deficiency › G6PD
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › favism
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › glucose-6-phosphate dehydrogenase (G6PD) deficiency
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › hemolytic › nonspherocytic › congenital or hereditary NEC › glucose-6-phosphate dehydrogenase deficiency
- Deficiency, deficient › glucose-6-phosphate dehydrogenase › anemia
- Favism (anemia)
- Poisoning (acute) › fava bean
- Toxicity › fava bean
Codes whose notes reference D55.0
- D75.AExcludes1
MS-DRG v44.0 grouping
All DRGs →Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.
MDC 16 · Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders
ICD-9-CM equivalent
Converter →- 282.2Anemias due to disorders of glutathione metabolismapproximate
From the CMS 2018 General Equivalence Mappings (GEMs), the final GEMs release.
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
- No changes since FY2016.
Common questions about D55.0
Is D55.0 billable?
- Yes. D55.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D55.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D55.0 as a principal diagnosis.
Is D55.0 a CC or MCC?
- No. D55.0 is neither a CC nor an MCC under MS-DRG v44.0.
What DRG does D55.0 group to?
- D55.0 is used in the MS-DRG v44.0 logic for MS-DRG 811 (Red Blood Cell Disorders with MCC) and MS-DRG 812 (Red Blood Cell Disorders without MCC). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.
What is the ICD-9 code for D55.0?
- The CMS General Equivalence Mappings map D55.0 to ICD-9-CM 282.2.