D57.8Other sickle-cell disorders

D57.8 is the ICD-10-CM diagnosis code for other sickle-cell disorders. It belongs to category D57 (sickle-cell disorders), block D55-D59 (hemolytic anemias) and chapter 3 (diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism). It is a header code, so it can't be reported by itself; one of its 2 subcodes must be used instead.

Within D57, choose D57.8 (Other sickle-cell disorders) only when documentation doesn't support a more specific option: Hb-SS disease with crisis (D57.0), sickle-cell disease without crisis (D57.1), Sickle-cell/Hb-C disease (D57.2), sickle-cell trait (D57.3) and sickle-cell thalassemia (D57.4).

To report this condition, pick the subcode that matches the documentation: D57.80 (without crisis) and D57.81 (with crisis).

Use an additional code for any associated fever (R50.81).

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.