D57.0Hb-SS disease with crisis

D57.0 is the ICD-10-CM diagnosis code for Hb-SS disease with crisis. It belongs to category D57 (sickle-cell disorders), block D55-D59 (hemolytic anemias) and chapter 3 (diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism). It is a header code, so it can't be reported by itself; one of its 6 subcodes must be used instead.

Within D57 (sickle-cell disorders), D57.0 is specifically for Hb-SS disease with crisis. Related codes cover sickle-cell disease without crisis (D57.1), Sickle-cell/Hb-C disease (D57.2), sickle-cell trait (D57.3), sickle-cell thalassemia (D57.4) and other sickle-cell disorders (D57.8).

To report this condition, pick the subcode that matches the documentation: D57.00 (unspecified), D57.01 (syndrome), D57.02 (sequestration), D57.03 (involvement), D57.04 (dactylitis) and D57.09 (with other specified complication).

Use an additional code for any associated fever (R50.81).

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.