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ICD-10-CM 2027 diagnosis code

E71.51Disorders of peroxisome biogenesis

Not billable — use a more specific code

E71.51 is a header code, so it can't be reported by itself. Choose one of the 3 more specific codes beneath it.

Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About E71.51

E71.51 is the ICD-10-CM diagnosis code for disorders of peroxisome biogenesis. It belongs to category E71 (disorders of branched-chain amino-acid metabolism and fatty-acid metabolism), block E70-E88 (metabolic disorders) and chapter 4 (endocrine, nutritional and metabolic diseases). It is a header code, so it can't be reported by itself; one of its 3 subcodes must be used instead.

Within E71.5 (peroxisomal disorders), E71.51 is specifically for disorders of peroxisome biogenesis. Related codes cover peroxisomal disorder, unspecified (E71.50), X-linked adrenoleukodystrophy (E71.52), other group 2 peroxisomal disorders (E71.53) and other peroxisomal disorders (E71.54).

To report this condition, pick the subcode that matches the documentation: E71.510 (syndrome), E71.511 (adrenoleukodystrophy) and E71.518 (biogenesis).

Don't report E71.51 together with the conditions in its Excludes1 note: Refsum's disease (G60.1).

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Specific codes under E71.51

Coding notes

Applicable toConditions and synonyms classified to this code
  • Group 1 peroxisomal disorders
Excludes1Not coded here — never report together with this code

Notes that apply from higher levels

Instructions written at a parent level also apply to E71.51.

› From E71.5 Peroxisomal disorders
Excludes1
  • Schilder's disease (G37.0)

Broader instructions also apply from E70-E88 Metabolic disorders and Chapter 4: Endocrine, nutritional and metabolic diseases.

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
  • No changes since FY2016.

Common questions about E71.51

Is E71.51 billable?

No. E71.51 is a header code. Report one of its more specific subcodes instead.