ICD-10-CM 2027
ICD-10 code for Aminoaciduria
Disorder of amino-acid metabolism, unspecified
From the official ICD-10-CM alphabetic index entry “Aminoaciduria”. Page updated September 29, 2026.
About coding Aminoaciduria
The ICD-10-CM code for Aminoaciduria is E72.9 (Disorder of amino-acid metabolism, unspecified).
Within E72, choose E72.9 (Disorder of amino-acid metabolism, unspecified) only when documentation doesn't support a more specific option: disorders of amino-acid transport (E72.0), disorders of sulfur-bearing amino-acid metabolism (E72.1), disorders of urea cycle metabolism (E72.2), disorders of lysine and hydroxylysine metabolism (E72.3), disorders of ornithine metabolism (E72.4), disorders of glycine metabolism (E72.5) and other specified disorders of amino-acid metabolism (E72.8).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Aminoaciduria ICD-10 codes
What is the ICD-10 code for Aminoaciduria?
- E72.9 — Disorder of amino-acid metabolism, unspecified.
Is E72.9 billable?
- Yes. E72.9 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E72.9 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E72.9 as a principal diagnosis.
Is E72.9 a CC or MCC?
- E72.9 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.