ICD-10-CM 2027
ICD-10 code for Hyperornithinemia
From the official ICD-10-CM alphabetic index entry “Hyperornithinemia”. Page updated September 29, 2026.
About coding Hyperornithinemia
The ICD-10-CM code for Hyperornithinemia is E72.4 (Disorders of ornithine metabolism).
Within E72 (other disorders of amino-acid metabolism), E72.4 is specifically for disorders of ornithine metabolism. Related codes cover disorders of amino-acid transport (E72.0), disorders of sulfur-bearing amino-acid metabolism (E72.1), disorders of urea cycle metabolism (E72.2), disorders of lysine and hydroxylysine metabolism (E72.3), disorders of glycine metabolism (E72.5), other specified disorders of amino-acid metabolism (E72.8) and disorder of amino-acid metabolism, unspecified (E72.9).
Don't report E72.4 together with the conditions in its Excludes1 note: hereditary choroidal dystrophy (H31.2-).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
Don't confuse with (Excludes1 for E72.4)
- hereditary choroidal dystrophy (H31.2-)
Common questions about Hyperornithinemia ICD-10 codes
What is the ICD-10 code for Hyperornithinemia?
- E72.4 — Disorders of ornithine metabolism.
Is E72.4 billable?
- Yes. E72.4 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E72.4 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E72.4 as a principal diagnosis.
Is E72.4 a CC or MCC?
- E72.4 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.