E83.824ABCC6 deficiency causing pseudoxanthoma elasticum

E83.824 is the ICD-10-CM diagnosis code for ABCC6 deficiency causing pseudoxanthoma elasticum. It belongs to category E83 (disorders of mineral metabolism), block E70-E88 (metabolic disorders) and chapter 4 (endocrine, nutritional and metabolic diseases). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within E83.82 (disorders of pyrophosphate metabolism), E83.824 is specifically for ABCC6 deficiency causing pseudoxanthoma elasticum. Related codes cover generalized arterial calcification of infancy with unspecified genetic causality (E83.820), ENPP1 deficiency causing generalized arterial calcification of infancy (E83.821), ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2 (E83.822), ABCC6 deficiency causing generalized arterial calcification of infancy (E83.823) and CD73 deficiency causing arterial calcification (E83.825).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It was added in FY2026, effective October 1, 2025.