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ICD-10-CM 2027

ICD-10 code for hemolytic anemia

D58.9

Hereditary hemolytic anemia, unspecified

✓ Billable / specificCC — complication/comorbidity

From the official ICD-10-CM alphabetic index entry “Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › hemolytic”. Page updated September 29, 2026.

About coding hemolytic anemia

The ICD-10-CM code for hemolytic anemia is D58.9 (Hereditary hemolytic anemia, unspecified). The official index lists 56 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on D58.9.

Within D58, choose D58.9 (Hereditary hemolytic anemia, unspecified) only when documentation doesn't support a more specific option: hereditary spherocytosis (D58.0), hereditary elliptocytosis (D58.1), other hemoglobinopathies (D58.2) and other specified hereditary hemolytic anemias (D58.8).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 811 (Red Blood Cell Disorders with MCC, relative weight 1.3988) and DRG 812 (Red Blood Cell Disorders without MCC, relative weight 0.9234), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

More specific hemolytic anemia codes (official index)

  • acquired D59.9 — Acquired hemolytic anemia, unspecified
  • with hemoglobinuria NEC D59.6 — Hemoglobinuria due to hemolysis from other external causes
  • autoimmune NEC D59.19 — Other autoimmune hemolytic anemia
  • infectious D59.4 — Other nonautoimmune hemolytic anemias
  • specified type NEC D59.8 — Other acquired hemolytic anemias
  • toxic D59.4 — Other nonautoimmune hemolytic anemias
  • acute D59.9 — Acquired hemolytic anemia, unspecified
  • due to enzyme deficiency specified type NEC D55.8 — Other anemias due to enzyme disorders
  • Lederer's D59.19 — Other autoimmune hemolytic anemia
  • autoimmune D59.10 — Autoimmune hemolytic anemia, unspecified
  • cold D59.12 — Cold autoimmune hemolytic anemia
  • drug-induced D59.0 — Drug-induced autoimmune hemolytic anemia
  • mixed D59.13 — Mixed type autoimmune hemolytic anemia
  • warm D59.11 — Warm autoimmune hemolytic anemia
  • chronic D58.9 — Hereditary hemolytic anemia, unspecified
  • idiopathic D59.9 — Acquired hemolytic anemia, unspecified
  • cold type (primary) (secondary) (symptomatic) D59.12 — Cold autoimmune hemolytic anemia
  • congenital (spherocytic)
  • due to
  • cardiac conditions D59.4 — Other nonautoimmune hemolytic anemias
  • drugs (nonautoimmune) D59.2 — Drug-induced nonautoimmune hemolytic anemia
  • autoimmune D59.0 — Drug-induced autoimmune hemolytic anemia
  • enzyme disorder D55.9 — Anemia due to enzyme disorder, unspecified
  • drug-induced D59.2 — Drug-induced nonautoimmune hemolytic anemia
  • presence of shunt or other internal prosthetic device D59.4 — Other nonautoimmune hemolytic anemias
  • familial D58.9 — Hereditary hemolytic anemia, unspecified
  • hereditary D58.9 — Hereditary hemolytic anemia, unspecified
  • due to enzyme disorder D55.9 — Anemia due to enzyme disorder, unspecified
  • specified type NEC D55.8 — Other anemias due to enzyme disorders
  • specified type NEC D58.8 — Other specified hereditary hemolytic anemias
  • idiopathic (chronic) D59.9 — Acquired hemolytic anemia, unspecified
  • mechanical D59.4 — Other nonautoimmune hemolytic anemias
  • microangiopathic D59.4 — Other nonautoimmune hemolytic anemias
  • mixed type (primary) (secondary) (symptomatic) D59.13 — Mixed type autoimmune hemolytic anemia
  • nonautoimmune D59.4 — Other nonautoimmune hemolytic anemias
  • drug-induced D59.2 — Drug-induced nonautoimmune hemolytic anemia
  • nonspherocytic
  • congenital or hereditary NEC D55.8 — Other anemias due to enzyme disorders
  • glucose-6-phosphate dehydrogenase deficiency D55.0 — Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency
  • pyruvate kinase deficiency D55.21 — Anemia due to pyruvate kinase deficiency
  • type
  • I D55.1 — Anemia due to other disorders of glutathione metabolism
  • II D55.29 — Anemia due to other disorders of glycolytic enzymes
  • type
  • I D55.1 — Anemia due to other disorders of glutathione metabolism
  • II D55.29 — Anemia due to other disorders of glycolytic enzymes
  • primary
  • autoimmune
  • cold type D59.12 — Cold autoimmune hemolytic anemia
  • mixed type D59.13 — Mixed type autoimmune hemolytic anemia
  • warm type D59.11 — Warm autoimmune hemolytic anemia
  • secondary D59.4 — Other nonautoimmune hemolytic anemias
  • autoimmune
  • cold type D59.12 — Cold autoimmune hemolytic anemia
  • mixed type D59.13 — Mixed type autoimmune hemolytic anemia
  • warm type D59.11 — Warm autoimmune hemolytic anemia
  • specified (hereditary) type NEC D58.8 — Other specified hereditary hemolytic anemias
  • Stransky-Regala type D58.8 — Other specified hereditary hemolytic anemias
  • symptomatic D59.4 — Other nonautoimmune hemolytic anemias
  • autoimmune
  • cold type D59.12 — Cold autoimmune hemolytic anemia
  • mixed type D59.13 — Mixed type autoimmune hemolytic anemia
  • warm type D59.11 — Warm autoimmune hemolytic anemia
  • toxic D59.4 — Other nonautoimmune hemolytic anemias
  • warm type (primary) (secondary) (symptomatic) D59.11 — Warm autoimmune hemolytic anemia

Common questions about hemolytic anemia ICD-10 codes

What is the ICD-10 code for hemolytic anemia?

D58.9 — Hereditary hemolytic anemia, unspecified. More specific codes apply when the documentation supports them: D59.9, D59.6, D59.19, D59.4 and others below.

What is the ICD-10 code for acquired hemolytic anemia?

D59.9 — Acquired hemolytic anemia, unspecified.

What is the ICD-10 code for acute hemolytic anemia?

D59.9 — Acquired hemolytic anemia, unspecified.

What is the ICD-10 code for autoimmune hemolytic anemia?

D59.10 — Autoimmune hemolytic anemia, unspecified.

What is the ICD-10 code for chronic hemolytic anemia?

D58.9 — Hereditary hemolytic anemia, unspecified.

What is the ICD-10 code for cold type hemolytic anemia?

D59.12 — Cold autoimmune hemolytic anemia.

What is the ICD-10 code for familial hemolytic anemia?

D58.9 — Hereditary hemolytic anemia, unspecified.

Is D58.9 billable?

Yes. D58.9 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can D58.9 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict D58.9 as a principal diagnosis.

Is D58.9 a CC or MCC?

D58.9 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.